Logo image
26-A-14770-ACC VIGOROUS EXERCISE IN CHILDREN WITH HYPERTROPHIC CARDIOMYOPATHY: SUBANALYSIS OF THE PROSPECTIVE, MULTINATIONAL LIFESTYLE AND EXERCISE IN HCM (LIVE-HCM) STUDY
Abstract   Peer reviewed

26-A-14770-ACC VIGOROUS EXERCISE IN CHILDREN WITH HYPERTROPHIC CARDIOMYOPATHY: SUBANALYSIS OF THE PROSPECTIVE, MULTINATIONAL LIFESTYLE AND EXERCISE IN HCM (LIVE-HCM) STUDY

Michael John Ackerman, Sharlene M. Day, Bradley S. Marino, Dominic J. Abrams, Barbara Ainsworth, Peter Aziz, Seshadri Balaji, Charles I. Berul, Martijn Bos, Richard J. Czosek, …
Journal of the American College of Cardiology, Vol.87(13 Supplement), pp.A1238-A1239
04/2026
DOI: 10.1016/j.jacc.2026.02.3050

View Online

Abstract

Background Data suggest that vigorous exercise does not carry excess risk for ventricular arrhythmia (VA) in adults with HCM. Risk in children is not described. Methods LIVE-HCM prospectively enrolled patients, age 8-60 years, from 42 sites in 5 countries, 5/2015-2/2019, including 222 children < 18 years. Children and parent-proxies answered physical activity and clinical events surveys every 6 mo for 3 yrs. Vigorous exercise was defined as > 6 METS for >60 hrs/yr. Blinded events committee adjudicated the composite endpoint (sudden death, cardiac arrest, VA treated by ICD, arrhythmic syncope). Only children with overt HCM, N= 167, were analyzed, as no phenotype negative child had an event. A noninferiority hypothesis (boundary of 1.5) between vigorous exercisers and others was tested via multivariable Cox regression analysis Results Among the 82 vigorous and 85 non-vigorous exercisers, 14 + 3 years, 61% male, 56% genotype positive, 16 individuals experienced the composite endpoint, 3 in the vigorous and 13 in non-vigorous groups, with rates per 1000 person-yrs for the vigorous of 12 (4-38) and for the non-vigorous 55 (32-94). All HRs met the pre-specified boundary for non-inferiority. Conclusion In this overt HCM pediatric cohort, most from expert HCM centers, children exercising vigorously did not experience a higher rate of death or life-threatening VA than the non-vigorous. These data may inform discussion between families and expert providers around exercise participation for children with HCM.

Details

Metrics

1 Record Views
Logo image