Journal article
A Case of Erdheim-Chester Disease Causing Secondary Sclerosing Cholangitis
ACG case reports journal, Vol.10(1), e00963
01/20/2023
DOI: 10.14309/crj.0000000000000963
PMCID: PMC9857465
PMID: 36699184
Abstract
Erdheim-Chester disease (ECD) is an exceedingly rare and aggressive disease characterized by foamy CD68 + CDa-histiocytic infiltration into multiple tissues and organs. Only 1,500 cases have been diagnosed since 1930 when ECD was first described. Biliary tract involvement of ECD has only been reported in the literature once. We report a case of ECD causing extrahepatic biliary obstruction without significant bile duct dilation, mimicking primary sclerosing cholangitis or IgG4 disease.
Details
- Title: Subtitle
- A Case of Erdheim-Chester Disease Causing Secondary Sclerosing Cholangitis
- Creators
- Vijayvardhan Kamalumpundi - Roy J. and Lucille A. Carver College of MedicineJohn Rieth - University of IowaHuy Tran - University of Iowa Hospitals and ClinicsMunish Ashat - University of Iowa Hospitals and ClinicsXiaocen Zhang - University of Iowa Hospitals and Clinics
- Resource Type
- Journal article
- Publication Details
- ACG case reports journal, Vol.10(1), e00963
- DOI
- 10.14309/crj.0000000000000963
- PMID
- 36699184
- PMCID
- PMC9857465
- NLM abbreviation
- ACG Case Rep J
- ISSN
- 2326-3253
- eISSN
- 2326-3253
- Publisher
- Wolters Kluwer
- Language
- English
- Date published
- 01/20/2023
- Academic Unit
- Gastroenterology and Hepatology; Internal Medicine
- Record Identifier
- 9984361569302771
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