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A de novo mutation in PRICKLE1 associated with myoclonic epilepsy and autism spectrum disorder
Journal article   Peer reviewed

A de novo mutation in PRICKLE1 associated with myoclonic epilepsy and autism spectrum disorder

Brittany P Todd and Alexander G Bassuk
Journal of neurogenetics, Vol.32(4), pp.313-315
10/02/2018
DOI: 10.1080/01677063.2018.1473862
PMCID: PMC6251753
PMID: 29790814

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Abstract

Homozygous recessive mutations in the PRICKLE1 gene were first described in three consanguineous families with myoclonic epilepsy. Subsequent studies have identified neurological abnormalities in humans and animal models with both heterozygous and homozygous mutations in PRICKLE1 orthologs. We describe a 7-year-old with a novel de novo missense mutation in PRICKLE1 associated with epilepsy, autism spectrum disorder and global developmental delay.
prickle epilepsy de novo mutation PRICKLE1 autism spectrum disorder

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