Journal article
Anesthetic implications of a pediatric patient with stiff skin syndrome: A case report
Pediatric anesthesia, Vol.30(10), pp.1149-1152
10/01/2020
DOI: 10.1111/pan.13989
PMID: 32761718
Abstract
Stiff skin syndrome is a rare genetic disorder that is present in infancy or early childhood. It is characterized by hard, inflexible skin and limited joint mobility making anesthetic management of these patients challenging. Their limited neck flexibility and chest wall rigidity make intubation and mask ventilation difficult. Intraoperative positioning can be challenging due to joint contractures and potential entrapment peripheral neuropathy. Even though peripheral intravenous access can be relatively easy, central venous cannulation may be problematic due to the hard skin overlying the entry sites. Our case report details the anesthetic management and considerations of a pediatric patient with stiff skin syndrome.
Details
- Title: Subtitle
- Anesthetic implications of a pediatric patient with stiff skin syndrome: A case report
- Creators
- Edgar E. Kiss - The University of Texas Southwestern Medical CenterGijo Alex - The University of Texas Southwestern Medical CenterNeethu Chandran - The University of Texas Southwestern Medical CenterPatrick Olomu - The University of Texas Southwestern Medical Center
- Resource Type
- Journal article
- Publication Details
- Pediatric anesthesia, Vol.30(10), pp.1149-1152
- Publisher
- Wiley
- DOI
- 10.1111/pan.13989
- PMID
- 32761718
- ISSN
- 1155-5645
- eISSN
- 1460-9592
- Number of pages
- 4
- Language
- English
- Date published
- 10/01/2020
- Academic Unit
- Anesthesia
- Record Identifier
- 9984656603202771
Metrics
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