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Autosomal dominant occipital cephalocele
Journal article   Peer reviewed

Autosomal dominant occipital cephalocele

Alexander G Bassuk, David McLone, Robin Bowman and John A Kessler
Neurology, Vol.62(10), pp.1888-1890
05/25/2004
DOI: 10.1212/01.WNL.0000125255.90915.5C
PMID: 15159504

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Abstract

The authors report the clinical and radiographic characteristics of a non-consanguineous Vietnamese kindred with an autosomal dominant form of occipital cephalocele. Affected family members all presented with occipital subscalp bulges at birth. Except for the proband, all individuals were developmentally normal with otherwise normal neurologic examinations. Unaffected family members, including obligate carriers, share no clinical characteristics, demonstrating incomplete penetrance.
Occipital Bone - abnormalities Agenesis of Corpus Callosum Humans Hydrocephalus - etiology Male Penetrance Diverticulum - genetics Magnetic Resonance Imaging Hydrocephalus - embryology Psychomotor Disorders - genetics Genes, Dominant Cerebral Ventricles - abnormalities Pedigree Adult Child Abnormalities, Multiple - genetics Infant, Newborn Encephalocele - genetics

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