Journal article
Chorea-amyotrophy with chronic hemolytic anemia: a variant of chorea-amyotrophy with acanthocytosis
Neurology, Vol.37(4), pp.645-649
1987
DOI: 10.1212/WNL.37.4.645
PMID: 3561776
Abstract
We studied two siblings with chorea and amyotrophy of adult onset and spherocytic hemolytic anemia. Autopsy revealed an atrophic striatum with iron deposition and spheroid bodies. Degeneration of the substantia nigra and spinal cord anterior horns was seen without iron deposition. The disorder seems to be a variant of the chorea-amyotrophy-acanthocytosis syndrome, and the pathology may account for evidence of parkinsonism and amyotrophy in that syndrome. Acanthocytosis may not be the only hematologic abnormality in this disorder.
Details
- Title: Subtitle
- Chorea-amyotrophy with chronic hemolytic anemia: a variant of chorea-amyotrophy with acanthocytosis
- Creators
- S. E SPENCER - Univ. Iowa coll. medicine, dep. neurology, Iowa City IA, United StatesF. O WALKER - Univ. Iowa coll. medicine, dep. neurology, Iowa City IA, United StatesS. A MOORE - Univ. Iowa coll. medicine, dep. neurology, Iowa City IA, United States
- Resource Type
- Journal article
- Publication Details
- Neurology, Vol.37(4), pp.645-649
- Publisher
- Lippincott Williams & Wilkins; Hagerstown, MD
- DOI
- 10.1212/WNL.37.4.645
- PMID
- 3561776
- ISSN
- 0028-3878
- eISSN
- 1526-632X
- Language
- English
- Date published
- 1987
- Academic Unit
- Pathology
- Record Identifier
- 9984047868002771
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