Journal article
Dermatomyositis Associated with Myelofibrosis following Polycythemia Vera
Case reports in hematology, Vol.2017(2017), pp.1-4
01/01/2017
DOI: 10.1155/2017/9091612
PMCID: PMC5474248
PMID: 28660085
Abstract
Dermatomyositis (DM) is a unique inflammatory myopathy with clinical findings of proximal muscle weakness, characteristic rash, and elevated muscle enzymes. The association of DM and malignancy, most commonly adenocarcinoma, is well known. There have been few case reports of primary myelofibrosis associated with DM. We present the case of a 69-year-old male with a history of polycythemia vera (PV) who developed proximal muscle weakness, dysphagia, and rash. He was found to have elevated creatinine kinase and skin biopsy was consistent with DM. Due to persistent pancytopenia a bone marrow biopsy was performed and showed postpolycythemic myelofibrosis. To our knowledge, this is the first case reported of this unique association.
Details
- Title: Subtitle
- Dermatomyositis Associated with Myelofibrosis following Polycythemia Vera
- Creators
- Naomi Fei - University of Iowa, Hematology, Oncology, and Blood & Marrow TransplantationSarah Sofka - West Virginia University Hospitals
- Resource Type
- Journal article
- Publication Details
- Case reports in hematology, Vol.2017(2017), pp.1-4
- DOI
- 10.1155/2017/9091612
- PMID
- 28660085
- PMCID
- PMC5474248
- NLM abbreviation
- Case Rep Hematol
- ISSN
- 2090-6560
- eISSN
- 2090-6579
- Publisher
- Hindawi
- Language
- English
- Date published
- 01/01/2017
- Academic Unit
- Hematology, Oncology, and Blood & Marrow Transplantation; Internal Medicine
- Record Identifier
- 9985166477502771
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