Logo image
Endovascular treatment of intrarenal aneurysms bleeding and angiomyolipomas in a patient with tuberous sclerosis and polycystic kidney disease
Journal article   Open access   Peer reviewed

Endovascular treatment of intrarenal aneurysms bleeding and angiomyolipomas in a patient with tuberous sclerosis and polycystic kidney disease

Túlio Leite, Lucas Vatanabe Pazinato, Maria Juliana de Aquino Vidal, Danielo de Freitas and Joaquim Maurício Da Motta Leal Filho
Jornal brasileiro de nefrologia, Vol.45(1), pp.111-115
01/01/2023
DOI: 10.1590/2175-8239-JBN-2021-0023
PMID: 34328493
url
https://doi.org/10.1590/2175-8239-JBN-2021-0023View
Published (Version of record) Open Access

Abstract

Tuberous sclerosis complex (TSC) and autosomal dominant polycystic kidney disease (ADPKD) are conditions related to renal failure that can rarely occur in association as a contiguous gene syndrome. Angiomyolipomas (AMLs) are renal tumors strongly related to TSC that may rupture and cause life-threatening bleedings. We present a patient with TSC, ADPKD, and renal AMLs with persistent hematuria requiring blood transfusion. The persistent hematuria was successfully treated through endovascular embolization, a minimally invasive nephron sparing technique.
Angiomyolipoma - complications Angiomyolipoma - therapy Hematuria - complications Hemorrhage - etiology Hemorrhage - therapy Humans Kidney Neoplasms - complications Polycystic Kidney Diseases - complications Polycystic Kidney Diseases - therapy Polycystic Kidney, Autosomal Dominant - complications Tuberous Sclerosis - genetics

Details

Metrics

Logo image