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Functional Role of the RNA-Binding Protein Rbm24a and Its Target sox2 in Microphthalmia
Journal article   Open access   Peer reviewed

Functional Role of the RNA-Binding Protein Rbm24a and Its Target sox2 in Microphthalmia

Lindy K Brastrom, C. Anthony Scott, Kai Wang and Diane C Slusarski
Biomedicines, Vol.9(2), p.100
01/21/2021
DOI: 10.3390/biomedicines9020100
PMID: 33494192
url
https://doi.org/10.3390/biomedicines9020100View
Published (Version of record) Open Access

Abstract

Congenital eye defects represent a large class of disorders affecting roughly 21 million children worldwide. Microphthalmia and anophthalmia are relatively common congenital defects, with approximately 20% of human cases caused by mutations in SOX2. Recently, we identified the RNA-binding motif protein 24a (Rbm24a) which binds to and regulates sox2 in zebrafish and mice. Here we show that morpholino knockdown of rbm24a leads to microphthalmia and visual impairment. By utilizing sequential injections, we demonstrate that addition of exogenous sox2 RNA to rbm24a -deplete embryos is sufficient to suppress morphological and visual defects. This research demonstrates a critical role for understanding the post-transcriptional regulation of genes needed for development.
vision sox2 microphthalmia post-transcriptional regulation visual assay RNA binding protein zebrafish rbm24a

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