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Genetic association study of exfoliation syndrome identifies a protective rare variant at LOXL1 and five new susceptibility loci
Journal article   Peer reviewed

Genetic association study of exfoliation syndrome identifies a protective rare variant at LOXL1 and five new susceptibility loci

Sasan Moghimi, Jost Jonas, Irma Järvelä, Jae Kang, Ryuichi Ideta, Rajesh Kumar, Patricio Schlottmann, Sarah Nelson, Daniella Bach-Holm, Shamira Perera, …
Nature Genetics, Vol.49(7), pp.993-1004
05/29/2017
DOI: 10.1038/ng.3875
PMID: 28553957
url
https://pasteur.hal.science/pasteur-02003892View
Open Access

Abstract

Exfoliation syndrome (XFS) is the commonest known risk factor for secondary glaucoma and a significant cause of blindness worldwide. Variants in two genes, LOXL1 and CACNA1A have been previously associated with XFS. To further elucidate the genetic basis of XFS, we collected a global sample of XFS cases to refine the association at LOXL1, which previously showed inconsistent results between populations,and to identify new variants associated with XFS. We identified a rare, protective allele at LOXL1 (p.407Phe, OR= 25, P=2.9 x 10-14) through deep resequencing of XFS cases and controls from 9 countries. This variant results in increased cellular adhesion strength compared to the wild-type (p.407Tyr) allele. A genome-wide association study (GWAS) of XFS cases and controls from 24 countries followed by replication in 18 countries identified seven genome-wide significant loci (P < 5 x 10-8). Index variants at the new loci map to chromosomes 13q12 (POMP), 11q23.3 (TMEM136), 6p21 (AGPAT1), 3p24 (RBMS3) and 5q23 (near SEMA6A). These findings provide biological insights into the pathology of XFS, and highlight a potential role for naturally occurring rare LOXL1 variants in disease biology.
Bioinformatics Computer Science Genetics Life Sciences Parasitology Virology Populations and Evolution Microbiology and Parasitology Quantitative Methods Santé publique et épidémiologie Human genetics

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