Gowers’ intrasyringeal hemorrhage associated with Chiari type I malformation in Noonan syndrome

Takafumi Mitsuhara; Satoshi Yamaguchi; Masaaki Takeda; Kaoru Kurisu

doi:10.4103/2152-7806.125546

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Gowers’ intrasyringeal hemorrhage associated with Chiari type I malformation in Noonan syndrome

Journal article

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Gowers’ intrasyringeal hemorrhage associated with Chiari type I malformation in Noonan syndrome

Takafumi Mitsuhara, Satoshi Yamaguchi, Masaaki Takeda and Kaoru Kurisu

Surgical neurology international, Vol.5(1), p.6

2014

DOI: 10.4103/2152-7806.125546

PMCID: PMC3927095

PMID: 24575321

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Abstract

Background: Idiopathic hemorrhage in a syrinx is a rare entity known as Gowers’ intrasyringeal hemorrhage. Bleeding confined to the syrinx cavity causes severe, sometimes acute, neurological deficits. We report a case of intrasyringeal hemorrhage into a preexisting lumbosacral syrinx associated with Chiari type I malformation. Case Description: A 39-year-old female with Noonan syndrome underwent foramen magnum decompression and a cervical syrinx-subarachnoid shunt for Chiari type I malformation-associated syringomyelia 7 years ago. She presented progressive gait deterioration and acute urinary dysfunction, indicating conus medullaris syndrome. Initial magnetic resonance imaging revealed massive hemorrhage in the intrasyringeal cavity of the conus medullaris. The patient underwent surgical removal of the intrasyringeal hematoma and her neurological symptoms improved postoperatively. Conclusion: Although Gowers’ intrasyringeal hemorrhage is rare, this entity should be taken into consideration in patients with syringomyelia showing acute neurological deterioration.

syringomyelia

intrasyringeal hemorrhage

Chiari type I malformation

Noonan syndrome

spinal disease

Case Report

Details

Title: Subtitle: Gowers’ intrasyringeal hemorrhage associated with Chiari type I malformation in Noonan syndrome
Creators: Takafumi Mitsuhara - Department of Neurosurgery, Graduate School of Biomedical Sciences, Hiroshima University, 1-2-3 Kasumi, Minami.ku, Hiroshima 734-8551, Japan
Satoshi Yamaguchi - Department of Neurosurgery, Graduate School of Biomedical Sciences, Hiroshima University, 1-2-3 Kasumi, Minami.ku, Hiroshima 734-8551, Japan
Masaaki Takeda - Department of Neurosurgery, Graduate School of Biomedical Sciences, Hiroshima University, 1-2-3 Kasumi, Minami.ku, Hiroshima 734-8551, Japan
Kaoru Kurisu - Department of Neurosurgery, Graduate School of Biomedical Sciences, Hiroshima University, 1-2-3 Kasumi, Minami.ku, Hiroshima 734-8551, Japan
Resource Type: Journal article
Publication Details: Surgical neurology international, Vol.5(1), p.6
DOI: 10.4103/2152-7806.125546
PMID: 24575321
PMCID: PMC3927095
NLM abbreviation: Surg Neurol Int
ISSN: 2152-7806
eISSN: 2152-7806
Publisher: Medknow Publications & Media Pvt Ltd; India
Language: English
Date published: 2014
Academic Unit: Neurosurgery
Record Identifier: 9984040388602771

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