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Identification of a Bardet-Biedl syndrome locus on chromosome 3 and evaluation of an efficient approach to homozygosity mapping
Journal article   Peer reviewed

Identification of a Bardet-Biedl syndrome locus on chromosome 3 and evaluation of an efficient approach to homozygosity mapping

Val C Sheffield, Rivka Carmi, Anne Kwitek-Black, Tatiana Rokhlina, Darryl Nishimura, Geoffrey M Duyk, Khalil Elbedour, Sara L Sunden and Edwin M Stone
Human molecular genetics, Vol.3(8), pp.1331-1335
08/1994
DOI: 10.1093/hmg/3.8.1331
PMID: 7987310

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Abstract

Bardet-Biedl syndrome is an autosomal recessive disorder characterized by mental retardation, obesity, retinitis pigmentosa, polydactyly and hypogonadism. Individuals with this disorder also have an increased incidence of hypertension, diabetes mellitus, and renal and cardiac anomalies. We previously identified a locus on chromosome 16 causing this disorder, and provided evidence that Bardet-Biedl syndrome is heterogeneous. In this study, we identify another Bardet-Biedl syndrome locus on chromosome 3 and confirm the non-allelic heterogeneity of this disorder in Bedouin populations. In addition, we demonstrate the feasibility of using pooled DNA samples from members of large kindreds as an efficient approach to homozygosity mapping.
DNA - genetics Chromosomes, Human, Pair 3 Homozygote Pedigree Humans Female Infant Male Chromosome Mapping Laurence-Moon Syndrome - genetics Evaluation Studies as Topic Genetic Linkage

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