Journal article
Imaging of lymphatic dysplasia in Noonan syndrome: Case studies and historical atlas
Lymphology, Vol.54(1), pp.23-40
01/01/2021
DOI: 10.2458/lymph.4679
PMID: 34506085
Abstract
To determine the historical use and utility of various lymphatic imaging modalities in Noonan syndrome (NS) patients, we performed a comprehensive literature review by collecting the published medical imaging of NS lymphatic dysplasias. We correlated imaging findings with clinical phenotypes and treatment. Our analysis of lymphatic imaging modalities provides an algorithmic approach to imaging and patient care across the spectrum of NS developmental defects. A total of 54 NS cases have been published since 1975. Using the observations reported in 15 reviewed publications, an association was made between disruptions in central lymphatic flow and poor clinical presentations/outcomes in NS patients.
Keywords: Noonan syndrome; algorithm; atlas; imaging; lymphangiography; lymphatic imaging; lymphatic vessel dysplasia; thoracic duct.
Details
- Title: Subtitle
- Imaging of lymphatic dysplasia in Noonan syndrome: Case studies and historical atlas
- Creators
- T CoxC VanceS DaleyC PapendieckH McGregorP H KuoM H Witte
- Resource Type
- Journal article
- Publication Details
- Lymphology, Vol.54(1), pp.23-40
- DOI
- 10.2458/lymph.4679
- PMID
- 34506085
- ISSN
- 0024-7766
- eISSN
- 2522-7963
- Language
- English
- Date published
- 01/01/2021
- Academic Unit
- Physical Therapy and Rehabilitation Science
- Record Identifier
- 9984294959702771
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