Infantile Scimitar Syndrome With Contralateral Pulmonary Vein Stenosis and Refractory Pulmonary Hypertension

Janelle Buysse; Ramya Deepthi Billa; Daniel McLennan; Ravi Ashwath; Aditya Badheka; Madhuradhar Chegondi

doi:10.7759/cureus.17203

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$Infantile Scimitar Syndrome With Contralateral Pulmonary Vein Stenosis and Refractory Pulmonary Hypertension$

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Infantile Scimitar Syndrome With Contralateral Pulmonary Vein Stenosis and Refractory Pulmonary Hypertension

Janelle Buysse, Ramya Deepthi Billa, Daniel McLennan, Ravi Ashwath, Aditya Badheka and Madhuradhar Chegondi

Curēus (Palo Alto, CA), Vol.13(8)

08/15/2021

DOI: 10.7759/cureus.17203

PMCID: PMC8439397

PMID: 34540431

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Abstract

Infantile scimitar syndrome is associated with pulmonary hypertension which can be difficult to manage. We present a three-month-old infant with scimitar syndrome, who eventually developed refractory pulmonary hypertension, posing a significant management challenge. Further workup demonstrated contralateral pulmonary vein stenosis, which is rarely described in scimitar syndrome. Our index case highlights the importance of follow-up cardiac catheterizations in these patients with severe pulmonary hypertension.

Cardiology

Pediatrics

cardiac catheterization

infantile scimitar syndrome

pulmonary hypertension

pulmonary vein stenosis

scimitar syndrome

Details

Title: Subtitle: Infantile Scimitar Syndrome With Contralateral Pulmonary Vein Stenosis and Refractory Pulmonary Hypertension
Creators: Janelle Buysse - University of Iowa
Ramya Deepthi Billa - University of Iowa
Daniel McLennan - University of Iowa
Ravi Ashwath - University of Iowa
Aditya Badheka - University of Iowa
Madhuradhar Chegondi - University of Iowa
Resource Type: Journal article
Publication Details: Curēus (Palo Alto, CA), Vol.13(8)
DOI: 10.7759/cureus.17203
PMID: 34540431
PMCID: PMC8439397
NLM abbreviation: Cureus
ISSN: 2168-8184
eISSN: 2168-8184
Publisher: Cureus
Language: English
Date published: 08/15/2021
Academic Unit: Radiology; Critical Care; Stead Family Department of Pediatrics
Record Identifier: 9984354524502771

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