Journal article
Infantile cranial fasciitis: case-based review and operative technique
Child's nervous system, Vol.33(6), pp.899-908
06/2017
DOI: 10.1007/s00381-017-3417-y
PMID: 28451777
Abstract
Cranial fasciitis (CF) is an uncommon benign primary lesion of the skull that typically affects the pediatric age group. Due to the rarity of CF, no prospective studies exist. Earliest description of this condition dates to 1980. The limited scientific and clinical literature regarding CF is dominated by case reports. For these reasons, questions pertaining to the true incidence, genetic risk factors, prognosis, and long-term outcome remain unanswered.
Clinically, CF presents as a firm, painless, growing scalp mass that is typically not considered in the differential diagnosis. Preoperative pathognomonic signs and symptoms are absent, and imaging features are often nonspecific. Treatment is typically through complete surgical resection, at which time histopathological examination confirms the diagnosis of CF. Reconstruction of the skull defect in the child is critical. Autograft techniques help maintain a rigid construct that integrates with the native skull while preserving its continued ability to grow. Generally, a good outcome is observed with complete resection.
We report a case of CF in an infant with emphasis on operative nuances and early follow-up results.
CF is a rare fibroproliferative disease that has a poorly defined incidence and long-term follow-up. Due to its locally invasive nature and nonspecific presentation, CF is often difficult to differentiate from malignancies and infections. Complete surgical resection is the best approach for diagnosis and cure. Its occult clinical presentation often allows it to achieve considerable growth, leaving a sizeable skull defect following resection. Since CF presents in the pediatric population, allograft reconstruction is preferred over titanium mesh or other synthetic materials to allow osseous integration and continued uninterrupted skull growth.
Details
- Title: Subtitle
- Infantile cranial fasciitis: case-based review and operative technique
- Creators
- Oliver E Flouty - Department of Neurosurgery, University of Iowa Hospitals and Clinics, Iowa city, IA, 52242, USAAnthony J Piscopo - Department of Biology, University of Iowa Hospitals and Clinics, Iowa city, IA, 52242, USAMarshall T Holland - Department of Neurosurgery, University of Iowa Hospitals and Clinics, Iowa city, IA, 52242, USAKingsley Abode-Iyamah - Department of Neurosurgery, University of Iowa Hospitals and Clinics, Iowa city, IA, 52242, USALeslie Bruch - Department of Pathology, University of Iowa Hospitals and Clinics, Iowa city, IA, 52242, USAArnold H Menezes - Department of Neurosurgery, University of Iowa Hospitals and Clinics, Iowa city, IA, 52242, USABrian J Dlouhy - Pappajohn Biomedical Institute, University of Iowa Carver College of Medicine, Iowa City, IA, USA. Brian-Dlouhy@uiowa.edu
- Resource Type
- Journal article
- Publication Details
- Child's nervous system, Vol.33(6), pp.899-908
- Publisher
- Germany
- DOI
- 10.1007/s00381-017-3417-y
- PMID
- 28451777
- ISSN
- 0256-7040
- eISSN
- 1433-0350
- Language
- English
- Date published
- 06/2017
- Academic Unit
- Stead Family Department of Pediatrics; Pathology; Iowa Neuroscience Institute; Neurosurgery; Otolaryngology
- Record Identifier
- 9984040270802771
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