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Inhibition of MCU forces extramitochondrial adaptations governing physiological and pathological stress responses in heart
Journal article   Open access   Peer reviewed

Inhibition of MCU forces extramitochondrial adaptations governing physiological and pathological stress responses in heart

Tyler P Rasmussen, Yuejin Wu, Mei-ling A Joiner, Olha M Koval, Nicholas R Wilson, Elizabeth D Luczak, Qinchuan Wang, Biyi Chen, Zhan Gao, Zhiyong Zhu, …
Proceedings of the National Academy of Sciences - PNAS, Vol.112(29), pp.9129-9134
07/21/2015
DOI: 10.1073/pnas.1504705112
PMCID: PMC4517214
PMID: 26153425
url
https://doi.org/10.1073/pnas.1504705112View
Published (Version of record) Open Access

Abstract

Myocardial mitochondrial Ca(2+) entry enables physiological stress responses but in excess promotes injury and death. However, tissue-specific in vivo systems for testing the role of mitochondrial Ca(2+) are lacking. We developed a mouse model with myocardial delimited transgenic expression of a dominant negative (DN) form of the mitochondrial Ca(2+) uniporter (MCU). DN-MCU mice lack MCU-mediated mitochondrial Ca(2+) entry in myocardium, but, surprisingly, isolated perfused hearts exhibited higher O2 consumption rates (OCR) and impaired pacing induced mechanical performance compared with wild-type (WT) littermate controls. In contrast, OCR in DN-MCU-permeabilized myocardial fibers or isolated mitochondria in low Ca(2+) were not increased compared with WT, suggesting that DN-MCU expression increased OCR by enhanced energetic demands related to extramitochondrial Ca(2+) homeostasis. Consistent with this, we found that DN-MCU ventricular cardiomyocytes exhibited elevated cytoplasmic [Ca(2+)] that was partially reversed by ATP dialysis, suggesting that metabolic defects arising from loss of MCU function impaired physiological intracellular Ca(2+) homeostasis. Mitochondrial Ca(2+) overload is thought to dissipate the inner mitochondrial membrane potential (ΔΨm) and enhance formation of reactive oxygen species (ROS) as a consequence of ischemia-reperfusion injury. Our data show that DN-MCU hearts had preserved ΔΨm and reduced ROS during ischemia reperfusion but were not protected from myocardial death compared with WT. Taken together, our findings show that chronic myocardial MCU inhibition leads to previously unanticipated compensatory changes that affect cytoplasmic Ca(2+) homeostasis, reprogram transcription, increase OCR, reduce performance, and prevent anticipated therapeutic responses to ischemia-reperfusion injury.
Adaptation, Physiological Blood Pressure Mitochondria, Heart - metabolism Calcium Channels - metabolism Diastole Calcium - metabolism Cytosol - drug effects Stress, Physiological Mitochondria, Heart - drug effects Cellular Reprogramming Genes, Dominant Myocardium - metabolism Electrocardiography Transcription, Genetic Sarcoplasmic Reticulum - metabolism Heart Ventricles - pathology Heart - physiopathology Oxygen Consumption Myocardium - pathology Cardiac Pacing, Artificial Animals Heart Ventricles - physiopathology Myocardial Reperfusion Prostaglandin-Endoperoxide Synthases - metabolism Glucose - metabolism Cytosol - metabolism Mice

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