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Leber congenital amaurosis due to CEP290mutations—severe vision impairment with a high unmet medical need: A Review
Journal article   Open access   Peer reviewed

Leber congenital amaurosis due to CEP290mutations—severe vision impairment with a high unmet medical need: A Review

Bart P Leroy, David G Birch, Jacque L Duncan, Byron L Lam, Robert K Koenekoop, Fernanda B. O Porto, Stephen R Russell and Aniz Girach
Retina (Philadelphia, Pa.), Vol.41(5), pp.898-907
05/2021
DOI: 10.1097/IAE.0000000000003133
PMID: 33595255
url
https://doi.org/10.1097/IAE.0000000000003133View
Published (Version of record) Open Access

Abstract

Supplemental Digital Content is Available in the Text. In this article, we review the clinical characteristics of Leber congenital amaurosis due to CEP290 mutations (LCA10) and its impact on patients and society. We discuss the challenges associated with differential diagnosis of LCA10, the significant burden of childhood visual impairment, and the investigational treatment strategies currently in development.
c2991+1655A>G CEP290 childhood blindness ciliopathy cone-rod dystrophy inherited retinal disease LCA10 Leber congenital amaurosis Review

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