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Motile cilia of human airway epithelia contain hedgehog signaling components that mediate noncanonical hedgehog signaling
Journal article   Open access   Peer reviewed

Motile cilia of human airway epithelia contain hedgehog signaling components that mediate noncanonical hedgehog signaling

Suifang Mao, Alok S Shah, Thomas O Moninger, Lynda S Ostedgaard, Lin Lu, Xiao Xiao Tang, Ian M Thornell, Leah R Reznikov, Sarah E Ernst, Philip H Karp, …
Proceedings of the National Academy of Sciences - PNAS, Vol.115(6), pp.1370-1375
02/06/2018
DOI: 10.1073/pnas.1719177115
PMCID: PMC5819449
PMID: 29358407
url
https://doi.org/10.1073/pnas.1719177115View
Published (Version of record) Open Access

Abstract

Differentiated airway epithelia produce sonic hedgehog (SHH), which is found in the thin layer of liquid covering the airway surface. Although previous studies showed that vertebrate HH signaling requires primary cilia, as airway epithelia mature, the cells lose primary cilia and produce hundreds of motile cilia. Thus, whether airway epithelia have apical receptors for SHH has remained unknown. We discovered that motile cilia on airway epithelial cells have HH signaling proteins, including patched and smoothened. These cilia also have proteins affecting cAMP-dependent signaling, including Gαi and adenylyl cyclase 5/6. Apical SHH decreases intracellular levels of cAMP, which reduces ciliary beat frequency and pH in airway surface liquid. These results suggest that apical SHH may mediate noncanonical HH signaling through motile cilia to dampen respiratory defenses at the contact point between the environment and the lung, perhaps counterbalancing processes that stimulate airway defenses.
Signal Transduction Cilia - physiology Epithelial Cells - metabolism Trachea - cytology Humans Cells, Cultured Hedgehog Proteins - metabolism Repressor Proteins - genetics Nuclear Proteins - metabolism Smoothened Receptor - metabolism Smoothened Receptor - genetics Cilia - metabolism Zinc Finger Protein Gli2 - metabolism Epithelial Cells - cytology Nuclear Proteins - genetics Bronchi - cytology Cyclic AMP - metabolism Repressor Proteins - metabolism Zinc Finger Protein Gli2 - genetics

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