Multimodality treatment of a massive cervicothoracic lymphaticvenous malformation in a 13-year-old boy

Cynthia Reyes; Taylor Parnall; Tania Kraai; Linda Butros; Anna Fabre; Jimmy Windsor; Jason McKee; Gresham Richter

doi:10.1016/j.epsc.2017.03.011

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Multimodality treatment of a massive cervicothoracic lymphaticvenous malformation in a 13-year-old boy

Journal article

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Multimodality treatment of a massive cervicothoracic lymphaticvenous malformation in a 13-year-old boy

Cynthia Reyes, Taylor Parnall, Tania Kraai, Linda Butros, Anna Fabre, Jimmy Windsor, Jason McKee and Gresham Richter

Journal of pediatric surgery case reports, Vol.21, pp.15-18

06/01/2017

DOI: 10.1016/j.epsc.2017.03.011

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Abstract

We report the multi-modality treatment of a massive cervicothoracic lymphatic-venous malformation (LVM) in a 13-year-old boy that was present at birth as a small cervical mass. At four years of age, sclerotherapy significantly reduced the size of the malformation but over subsequent years the mass increased dramatically in size and resulted in a consumptive coagulopathy and limited left shoulder function. Treatment with sildenafil was without effect. The consumptive coagulopathy improved with subcutaneous enoxaparin. A multi-disciplinary team excised part of the mass when he was 11 years old. After surgery, gradual enlargement of the mass and rise in d-dimer prompted treatment with sirolimus. Two sessions of sclerotherapy arrested enlargement of the mass. Multi-modality treatment resulted in a marked reduction of the LVM in the child. However, enlargement of the mass and further treatment is anticipated as a cure has not yet been found. Published by Elsevier Inc. This is an open access article under the CC BY-NC-ND license

Life Sciences & Biomedicine

Pediatrics

Science & Technology

Details

Title: Subtitle: Multimodality treatment of a massive cervicothoracic lymphaticvenous malformation in a 13-year-old boy
Creators: Cynthia Reyes - University of New Mexico
Taylor Parnall - University of New Mexico
Tania Kraai - University of New Mexico
Linda Butros - University of New Mexico
Anna Fabre - University of New Mexico
Jimmy Windsor - University of New Mexico
Jason McKee - University of New Mexico
Gresham Richter - Arkansas Children's Hospital
Resource Type: Journal article
Publication Details: Journal of pediatric surgery case reports, Vol.21, pp.15-18
DOI: 10.1016/j.epsc.2017.03.011
ISSN: 2213-5766
eISSN: 2213-5766
Publisher: Elsevier
Number of pages: 4
Grant note: Dean of the University of New Mexico Health Science Center Mexico Governor Susanna Martinez
Language: English
Date published: 06/01/2017
Academic Unit: Anesthesia
Record Identifier: 9984296138402771

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