Journal article
Multisystem Imaging Findings of Cystic Fibrosis in Adults: Recognizing Typical and Atypical Patterns of Disease
American journal of roentgenology (1976), Vol.209(1), pp.3-18
07/2017
DOI: 10.2214/AJR.16.17462
PMID: 28639921
Abstract
There is an expanding and increasingly heterogeneous population of adult patients with cystic fibrosis (CF). Although CF is usually diagnosed in children with progressive multisystem involvement, up to 7% of CF cases are currently diagnosed de novo in adults with subtle manifestations distinct from the typical features of classic CF. The purpose of this article is to present the wide spectrum of CF in adults, including both classic and nonclassic variants, with an emphasis on the nonclassic imaging findings.
Recurrent pancreatitis, chronic sinusitis, and congenital bilateral absence of the vas deferens (CBAVD) are several of the ways in which CF is identified in adult patients with relatively rare mutations and with overall milder manifestations. It is important for radiologists to recognize the wide spectrum of CF to optimally monitor disease progression and response to therapeutic interventions in distinct adult patient populations.
Details
- Title: Subtitle
- Multisystem Imaging Findings of Cystic Fibrosis in Adults: Recognizing Typical and Atypical Patterns of Disease
- Creators
- Sarah Averill - University of Iowa, RadiologyMeghan G Lubner - 1 Department of Radiology, University of Wisconsin School of Medicine & Public Health, 600 Highland Ave, E3/311 Clinical Science Center, Madison, WI 53792-3252Christine O Menias - 2 Department of Radiology, Mayo Clinic Arizona, Scottsdale, AZSanjeev Bhalla - 3 Mallinckrodt Institute of Radiology, Washington University in St. Louis, St. Louis, MOVincent M Mellnick - 3 Mallinckrodt Institute of Radiology, Washington University in St. Louis, St. Louis, MOTabassum A Kennedy - 1 Department of Radiology, University of Wisconsin School of Medicine & Public Health, 600 Highland Ave, E3/311 Clinical Science Center, Madison, WI 53792-3252Perry J Pickhardt - 1 Department of Radiology, University of Wisconsin School of Medicine & Public Health, 600 Highland Ave, E3/311 Clinical Science Center, Madison, WI 53792-3252
- Resource Type
- Journal article
- Publication Details
- American journal of roentgenology (1976), Vol.209(1), pp.3-18
- DOI
- 10.2214/AJR.16.17462
- PMID
- 28639921
- ISSN
- 0361-803X
- eISSN
- 1546-3141
- Language
- English
- Date published
- 07/2017
- Academic Unit
- Radiology
- Record Identifier
- 9984131872702771
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