Native atrial septal restriction after Fontan palliation successfully treated with transcatheter Diabolo stent

Osamah Aldoss; Benjamin E Reinking; Abhay Divekar

doi:10.4103/0974-2069.171411

Back

Native atrial septal restriction after Fontan palliation successfully treated with transcatheter Diabolo stent

Journal article

Open access

Peer reviewed

Native atrial septal restriction after Fontan palliation successfully treated with transcatheter Diabolo stent

Osamah Aldoss, Benjamin E Reinking and Abhay Divekar

Annals of pediatric cardiology, Vol.9(1), pp.49-52

2016

DOI: 10.4103/0974-2069.171411

PMCID: PMC4782469

PMID: 27011693

Files and links (1)

url

https://doi.org/10.4103/0974-2069.171411View

Published (Version of record) Open Access

Abstract

A 6-year-old male child born with hypoplastic left heart syndrome (HLHS) was palliated with an extracardiac nonfenestrated Fontan procedure (18-mm Gore-Tex tube graft). He developed low-pressure (mean Fontan pressure 10 mmHg) protein-losing enteropathy 6 months after Fontan palliation. After initially responding to medical therapy and transcatheter pulmonary artery stent implantation, he developed medically refractory protein-losing enteropathy. At this time, his transthoracic echocardiogram showed new restriction across his native atrial septum with an 8 mmHg mean gradient. Cardiac catheterization now showed high-pressure (mean Fontan pressure 18-20 mmHg) protein-losing enteropathy and a new 6 mmHg mean gradient across the atrial septum. To avoid cardiopulmonary bypass, he underwent successful transcatheter relief of atrial septal restriction and creation of a fenestration with rapid clinical and biochemical improvement of his protein-losing enteropathy.

Diabolo stent

hypoplastic left heart syndrome (HLHS)

atrial septal restriction

Case Report

Details

Title: Subtitle: Native atrial septal restriction after Fontan palliation successfully treated with transcatheter Diabolo stent
Creators: Osamah Aldoss - Department of Pediatrics, Division of Pediatric Cardiology, University of Iowa Children's Hospital, Iowa City, Iowa, USA
Benjamin E Reinking - Department of Pediatrics, Division of Pediatric Cardiology, University of Iowa Children's Hospital, Iowa City, Iowa, USA
Abhay Divekar - Department of Pediatrics, Division of Pediatric Cardiology, University of Iowa Children's Hospital, Iowa City, Iowa, USA
Resource Type: Journal article
Publication Details: Annals of pediatric cardiology, Vol.9(1), pp.49-52
DOI: 10.4103/0974-2069.171411
PMID: 27011693
PMCID: PMC4782469
NLM abbreviation: Ann Pediatr Cardiol
ISSN: 0974-2069
eISSN: 0974-5149
Publisher: Medknow Publications & Media Pvt Ltd
Language: English
Date published: 2016
Academic Unit: Cardiology; Stead Family Department of Pediatrics
Record Identifier: 9984093211002771

Metrics

30 Record Views

4 Times Cited - Web of Science