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New mesomelic dysplasia with absent fibulae and triangular tibiae
Journal article   Peer reviewed

New mesomelic dysplasia with absent fibulae and triangular tibiae

Ravi Savarirayan, Valérie Cormier‐Daire, Cynthia J Curry, Marcus B Nashelsky, Valerie Rappaport, David L Rimoin and Ralph S Lachman
American journal of medical genetics, Vol.94(1), pp.59-63
09/04/2000
DOI: 10.1002/1096-8628(20000904)94:1<59::AID-AJMG12>3.0.CO;2-2
PMID: 10982484

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Abstract

We report on two unrelated, sporadic cases of a mesomelic dysplasia characterized by absence of fibulae and severely hypoplastic, triangular‐shaped tibiae. Moderate mesomelic shortness was present in the upper limbs with proximal widening of the ulnae. There was also axial skeletal involvement in both cases, characterized radiographically by an abnormal pelvis and marked bilateral glenoid hypoplasia. These cases appear to represent a new form of mesomelic dysplasia distinct from those previously delineated. Am. J. Med. Genet. 94:59–63, 2000. © 2000 Wiley‐Liss, Inc.
mesomelic dysplasia triangular‐shaped tibiae skeletal dysplasia absent fibulae

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