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Presentation and Treatment of Poland Anomaly
Journal article   Open access   Peer reviewed

Presentation and Treatment of Poland Anomaly

Joseph A Buckwalter V and Apurva S Shah
Hand (New York, N.Y.), Vol.11(4), pp.389-395
12/2016
DOI: 10.1177/1558944716647355
PMCID: PMC5256661
PMID: 28149203
url
https://doi.org/10.1177/1558944716647355View
Published (Version of record) Open Access

Abstract

Background: Poland anomaly is a sporadic, phenotypically variable congenital condition usually characterized by unilateral pectoral muscle agenesis and ipsilateral hand deformity. Methods: A comprehensive review of the medical literature on Poland anomaly was performed using a Medline search. Results: Poland anomaly is a sporadic, phenotypically variable congenital condition usually characterized by unilateral, simple syndactyly with ipsilateral limb hypoplasia and pectoralis muscle agenesis. Operative management of syndactyly in Poland anomaly is determined by the severity of hand involvement and the resulting anatomical dysfunction. Syndactyly reconstruction is recommended in all but the mildest cases because most patients with Poland anomaly have notable brachydactyly, and digital separation can improve functional length. Conclusions: Improved understanding the etiology and presentation of Poland anomaly can improve clinician recognition and management of this rare congenital condition.
symbrachydactyly congenital hand Reviews Poland anomaly pectoral agenesis Poland syndrome

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