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Pretibial dystrophic epidermolysis bullosa associated with aberrant exon splicing of type VII collagen
Journal article   Open access   Peer reviewed

Pretibial dystrophic epidermolysis bullosa associated with aberrant exon splicing of type VII collagen

Patricia Richey, Melia Holt, Sydney Crotts and Ali Jabbari
JAAD Case Reports, Vol.5(9), pp.779-781
09/01/2019
DOI: 10.1016/j.jdcr.2019.06.032
PMID: 31516996
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Published (Version of record) Open Access CC BY-NC-ND V4.0
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https://doi.org/10.1016/j.jdcr.2019.06.032View
Published (Version of record) JAAD Case Reports 2019;5:779-81

Abstract

Introduction Epidermolysis bullosa (EB) is a group of genetic disorders characterized by blisters and erosions/ulcerations in response to otherwise benign mechanical forces applied to the skin. Pretibial epidermolysis bullosa (PEB) is a form of EB that most often presents with blistering, ulceration, scarring, and milia localized to the bilateral legs. We report a case of man in his 50s presenting with blistering and scarring of his bilateral legs caused by PEB found to be associated with a mutation in COL7A1 that results in exon skipping.
lower extremity ulcers epidermolysis bullosa exon skipping RNA splicing

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