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Rating Scales for Cognition in Huntington's Disease: Critique and Recommendations
Journal article   Open access   Peer reviewed

Rating Scales for Cognition in Huntington's Disease: Critique and Recommendations

Tiago A. Mestre, Anne-Catherine Bachoud-Levi, Johan Marinus, Julie C. Stout, Jane S. Paulsen, Peter Como, Kevin Duff, Cristina Sampaio, Christopher G. Goetz, Esther Cubo, …
Movement disorders, Vol.33(2), pp.187-195
02/01/2018
DOI: 10.1002/mds.27227
PMCID: PMC10080408
PMID: 29278291
url
https://pmc.ncbi.nlm.nih.gov/articles/PMC10080408/pdf/nihms-1870114.pdfView
Open Access

Abstract

Cognitive impairment is one of the main features of Huntington's disease and is present across the disease spectrum. As part of the International Parkinson's Disease and Movement Disorder Society-sponsored project to review all clinical rating scales used in Huntington's disease, a systematic review of the literature was performed to identify cognitive scales used in Huntington's disease and make recommendations for their use. A total of 17 cognitive scales were identified and evaluated. None of the scales met criteria for a recommended status. For assessing severity of cognitive dysfunction, the Montreal Cognitive Assessment was recommended with caveats. The UHDRS Cognitive Assessment, the UHDRS-For Advanced Patients cognitive section, the Alzheimer's Disease Assessment Scale-Cognitive Subscale, the Frontal Assessment Battery, the Mattis Dementia Rating Scale, the Mini-Mental State Examination, and the Repeatable Battery for the Assessment of Neuropsychological Status were suggested for evaluating severity of cognitive impairment. The MoCA was suggested as a screening tool for cognitive impairment. The major challenge in the assessment of cognition in Huntington's disease is the lack of a formal definition of dementia and/or mild cognitive impairment in this disease. The committee concluded that there is a need to further validate currently available cognitive scales in Huntington's disease, but that it is premature to recommend the development of new scales. Recently developed Huntington's disease-specific scales, such as the Huntington's Disease-Cognitive Assessment Battery, hold promise but require the completion of more comprehensive clinimetric development. (c) 2017 International Parkinson and Movement Disorder Society
Clinical Neurology Life Sciences & Biomedicine Neurosciences & Neurology Science & Technology

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