Severe Cherubism Treated with Curettage, Osteotomy, and Bony Repositioning: A Case Series of Three Patients

Whitney Moss; Giovanna Pires; Rehan Zahid; Richard Tyrell; Irfan Rhemtulla; Barbu Gociman

doi:10.1097/GOX.0000000000004079

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Severe Cherubism Treated with Curettage, Osteotomy, and Bony Repositioning: A Case Series of Three Patients

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Severe Cherubism Treated with Curettage, Osteotomy, and Bony Repositioning: A Case Series of Three Patients

Whitney Moss, Giovanna Pires, Rehan Zahid, Richard Tyrell, Irfan Rhemtulla and Barbu Gociman

Plastic and reconstructive surgery. Global open, Vol.10(1), p.E4079

01/27/2022

DOI: 10.1097/GOX.0000000000004079

PMCID: PMC8849314

PMID: 35186633

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Abstract

Cherubism is a rare, autosomal dominant condition characterized by the replacement of medullary bone by fibro-osseous lesions, predominantly in the bilateral maxillae and/or mandibles. The clinical presentation of cherubism can vary widely, from clinically undetectable to severe facial disfigurement. Although there are no established management guidelines for this condition, conservative management with observation is typically favored in most cases due to the possibility of spontaneous regression following puberty. In this article, we present three cases of moderate to severe cherubism managed with early surgical intervention utilizing curettage and osteotomy followed by bony repositioning. We aimed to show the feasibility and safety of this minimally invasive surgical technique in the management of moderate to severe cases of cherubism to provide improvement in patient quality of life, aesthetics, and function while also possibly mitigating the need for later reconstructive surgery.

Case Report

Craniofacial/Pediatric

Details

Title: Subtitle: Severe Cherubism Treated with Curettage, Osteotomy, and Bony Repositioning: A Case Series of Three Patients
Creators: Whitney Moss - University of Utah
Giovanna Pires - University of Utah
Rehan Zahid - University of Utah
Richard Tyrell - Temple University
Irfan Rhemtulla - University of Utah
Barbu Gociman - University of Utah
Resource Type: Journal article
Publication Details: Plastic and reconstructive surgery. Global open, Vol.10(1), p.E4079
Publisher: Lippincott Williams & Wilkins
DOI: 10.1097/GOX.0000000000004079
PMID: 35186633
PMCID: PMC8849314
ISSN: 2169-7574
eISSN: 2169-7574
Language: English
Date published: 01/27/2022
Academic Unit: Surgery
Record Identifier: 9984701654802771

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