Journal article
Stromal Tumor of the Sex Cord in a Woman with Testicular Feminization Syndrome: Imaging Features
American journal of roentgenology (1976), Vol.178(6), pp.1496-1498
06/2002
DOI: 10.2214/ajr.178.6.1781496
PMID: 12034627
Abstract
Testicular feminization is a form of male pseudohermaphroditism that is inherited as a sex-linked recessive disorder. It is characterized by androgen insensitivity resulting from an absence or qualitative abnormality of the cytosol receptor for androgens [1]. Despite having a male genotype, most patients with testicular feminization (androgen insensitivity) syndrome are asymptomatic and function as normal, although sterile, females. Undescended testes have a well-recognized propensity for tumoral proliferation, and the risk of gonadal malignancies increases with age [2]. Although the diagnosis of androgen insensitivity syndrome is based primarily on clinical features, imaging modalities may provide complementary findings. Nevertheless, the imaging findings in patients with testicular feminization syndrome have been poorly documented. We describe the imaging features in a 54-year-old patient with testicular feminization syndrome in whom a stromal tumor of the sex cord developed within an intraabdominal testis. To our knowledge, this case is the first to be reported with CT and MR imaging documentation.
Details
- Title: Subtitle
- Stromal Tumor of the Sex Cord in a Woman with Testicular Feminization Syndrome: Imaging Features
- Creators
- Nevzat Karabulut - Pamukkale UniversityAysun Karabulut - Denizli Devlet HastanesiEmre Pakdemirli - Pamukkale UniversityNuran Sabir - Pamukkale UniversitySeyide Kara Soysal - Pamukkale UniversityM. Emin Soysal - Pamukkale University
- Resource Type
- Journal article
- Publication Details
- American journal of roentgenology (1976), Vol.178(6), pp.1496-1498
- Publisher
- AMER ROENTGEN RAY SOC; RESTON
- DOI
- 10.2214/ajr.178.6.1781496
- PMID
- 12034627
- ISSN
- 0361-803X
- eISSN
- 1546-3141
- Language
- English
- Date published
- 06/2002
- Academic Unit
- Radiology
- Record Identifier
- 9984697638202771
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