Journal article
Tetralogy of Fallot with absent pulmonary valve syndrome; appropriate surgical strategies
Journal of the Pakistan Medical Association, Vol.65(5), pp.467-472
05/31/2015
PMID: 26028378
Abstract
Objective: To evaluate patients presenting with Tetralogy of Fallot with absent pulmonary valve syndrome to a tertiary care hospital and their surgical management.
Methods: The retrospective study was conducted at Congenital Cardiac Services, Aga Khan University Hospital, Karachi, Pakistan, and comprised data of Tetralogy of Fallot patients between April 2007 and June 2012. Data was analysed together with follow-up echocardiography. Variables assessed included demographics, imaging, operative technique, complications, post-operative recovery and follow-up echocardiography. SPSS 17 was used for statistical analysis.
Results: Of the 204 patients, 6(3%) had undergone surgical correction for Tetralogy of Fallot with absent pulmonary valve syndrome. All 6(100%) patients underwent complete repair. Median age for surgery was 8.5 years (range: 0.5-29 years). Of the different surgical strategies used, Contegra and Bioprosthetic valve placement had satisfactory outcome with minimal gradient at Right Ventricular Outflow Tract, good ventricular function and mild valvular regurgitation. One (16.6%) patient with Trans Annular Patch developed post-operative Right Ventricle Outflow Tract gradient of 80mmHg with moderate pulmonary regurgitation. One (16.6%) patient with monocusp valve developed free pulmonary regurgitation at 6 months. The other 4(66.6%) patients are currently free from any complications or re-intervention.
Conclusion: Early surgery is preferred in symptomatic patients. The repair depends upon achieving integrity of pulmonary circulation which is best achieved by using right ventricle to pulmonary artery conduit or inserting a pulmonary valve.
Details
- Title: Subtitle
- Tetralogy of Fallot with absent pulmonary valve syndrome; appropriate surgical strategies
- Creators
- Fatima Shahid - University of KarachiMaria Tariq Siddiqui - University of KarachiMuhammad Muneer Amanullah - Aga Khan University
- Resource Type
- Journal article
- Publication Details
- Journal of the Pakistan Medical Association, Vol.65(5), pp.467-472
- PMID
- 26028378
- NLM abbreviation
- J Pak Med Assoc
- ISSN
- 0030-9982
- Publisher
- Pakistan Medical Assoc
- Number of pages
- 6
- Language
- English
- Date published
- 05/31/2015
- Academic Unit
- Internal Medicine
- Record Identifier
- 9984848421602771
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