Journal article
Xanthoma Disseminatum: An Unusual Histiocytosis Syndrome
Journal of pediatric hematology/oncology, Vol.10(3), pp.252-257
1988
DOI: 10.1097/00043426-198823000-00014
PMID: 3140686
Abstract
The histiocytoses are a diverse group of illnesses that present a variety of diagnostic and therapeutic dilemmas. In this article, we describe the case of an 8-year-old boy with xanthoma disseminatum, a histiocytic disorder involving the skin, eyes, and brain. In our discussion, we have emphasized the clinical, pathologic, and radiographic features that distinguish this entity from clinically similar juvenile xanthogranuloma and Langerhans' cell histiocytoses (histiocytosis X) such as the Hand-Schuller-Christian syndrome. The importance of differentiating the various histiocytoses, in view of their varying natural histories and therapeutic responsiveness, is reviewed in relation to the new classification system for these disorders proposed by the Histiocyte Society.
Details
- Title: Subtitle
- Xanthoma Disseminatum: An Unusual Histiocytosis Syndrome
- Creators
- Roger H GillerRobert FolbergRonald V KeechWarren W PietteYutaka Sato
- Resource Type
- Journal article
- Publication Details
- Journal of pediatric hematology/oncology, Vol.10(3), pp.252-257
- DOI
- 10.1097/00043426-198823000-00014
- PMID
- 3140686
- ISSN
- 1077-4114
- eISSN
- 1536-3678
- Language
- English
- Date published
- 1988
- Academic Unit
- Radiology; Stead Family Department of Pediatrics
- Record Identifier
- 9984051705402771
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